childhood disintegrative disorder
PAEDIATRIC NEUROLOGY
An uncommon–1.7/105–idiopathic condition affecting children which is characterised by normal development followed by a deterioration of developmental milestones in language, social function, and motor skills.
Note: Childhood disintegrateive disorder is included in the American Psychiatriac Association’s DSM-5 under the umbrella term of autism spectrum disorder.
Case-defining features: 2 of the following 6 functional areas:
• Expressive language skills
• Language comprehension
• Social skills
• Self care
• Bowel and bladder control
• Play skills
• Motor skills
Impairment in 2+ of the following 3 areas:
• Social interaction
• Communication
• Repetitive behaviour & interests
Aetiology Unknown; may be associated with lipid storage diseases, subacute sclerosing panencephalitis, tuberous sclerosis
Management As for autism: behaviour therapy, environmental (sensory enrichment) therapy, medications–e.g., antipsychotics, anticonvulsants
Synonyms Dementia infantilis, disintegrative psychosis, Heller syndrome
Reference https://en.wikipedia.org/wiki/Childhood_disintegrative_disorder
http://www.dsm5.org/documents/changes%20from%20dsm-iv-tr%20to%20dsm-5.pdf
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